Clinical Practice Guidelines for nutritional management of Cystic Fibrosis patients (GPC-CF)

Authors

  • María Garriga Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Ramón y Cajal de Madrid
  • Adriana Horrisberger Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística
  • Arantza Ruiz de las Heras de la Hera Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Complejo Hospitalario de Navarra- Pamplona.
  • Natalia Catalán Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística
  • Gloria Fernández Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística
  • Marta Suárez Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Central de Asturias.
  • Nuria Porras Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Regional Universitario Carlos Haya de Málaga.
  • Laura Monje Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Marqués de Valdecilla, Santander

DOI:

https://doi.org/10.14306/renhyd.21.1.229

Keywords:

Cystic Fibrosis, Diet Therapy, Practice Guidelines as Topic

Abstract

Cystic fibrosis (CF) is a multiorgan, hereditary, autosomal and recessive disease whose most frequent problems are related to alterations of the lungs and exocrine pancreas. The objective of this guide is to establish guidelines in clinical practice for the nutritional management of people with CF. Recommendations on the evaluation of clinical and nutritional status (anamnesis, physical examination, body composition, biochemistry, lung function, nutritional nutrition and Weight loss, nutritional nutrition, vitamin and mineral supplementation, treatment of pancreatic insufficiency, diabetes, and liver disease) and other circumstances (pregnancy, lactation, and lung transplantation) also can be found in this guide. The guideline has been developed through a simple review by a group of experts who made decisions by consensus to assist in the decision making of professionals involved in patient care. This guide has been reviewed and approved by the Scientific Committee of the Spanish Foundation of Dieticians and Nutritionists (FEDN). This guide is not intended to be mandatory nor to replace the clinical judgment of health personnel.

Author Biographies

María Garriga, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Ramón y Cajal de Madrid

Grado en Nutrición Humana y Dietética por la Universidad de Navarra

Licenciada en Ciencia y Tecnología de Alimentos por la Universidad Complutense de Madrid

Doctora en Ciencias de la Salud por la Univesidad de Alcalá

Coordinadora del Grupo Español de Dietistas/ Nutricionistas de Fibrosis Quística (GEDN/ FQ).

Trabajo como Dietista-Nutricionista en el Hospital Universitario Ramón y Cajal. Servicio de Endocrinología y Nutrición. Servicio de Pediatría. Unidad de Fibrosis Quística

Adriana Horrisberger, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística

Licenciada en Nutrición por la Universidad Nacional de Córdoba (Argentina).

Miembro del Grupo Español de Dietistas/ Nutricionistas de Fibrosis Quística (GEDN/ FQ).

Arantza Ruiz de las Heras de la Hera, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Complejo Hospitalario de Navarra- Pamplona.

 

Dietista-Nutricionista
Miembro de la Sección de Nutrición Clínica y Dietética y de la Unidad de Nutrición Pediátrica Hospitalaria del Complejo Hospitalario de Navarra.
Miembro del Grupo Español de Dietistas-Nutricionistas de Fibrosis Quística (GEDN/FQ).

 

Natalia Catalán, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística

Ex Dietista-Nutricionista de la Unidad de Fibrosis Quística del Hospital Sant Joan de Déu, Barcelona.
Miembro del Grupo Español de Dietistas/ Nutricionistas de Fibrosis Quística (GEDN/ FQ).

Gloria Fernández, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística

Dietista-Nutricionista, especializada en Nutrición Pediátrica por la Universidad de Henri Poincaré (Francia).
Miembro del Grupo Español de Dietistas/ Nutricionistas de Fibrosis Quística (GEDN/ FQ)

Marta Suárez, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Central de Asturias.

Dietista-Nutricionista. Lic. en Ciencia y Tecnología de los Alimentos. Unidad de Gastroenterología, Hepatología, Nutrición y Metabolismo Pediátrico. Hospital Universitario Central de Asturias.Miembro del Grupo Español de Dietistas-Nutricionistas de Fibrosis Quística (GEDN/FQ).

Laura Monje, Grupo Español de Dietistas-Nutricionistas de la Fibrosis Quística (GEDN/FQ), Federación Española de Fibrosis Quística. Hospital Universitario Marqués de Valdecilla, Santander

Doctora en Ciencias de la Salud (Facultad de Medicina) por la Universidad de Cantabria

Graduada y Diplomada en Nutrición Humana y Dietética por la Universidad de Navarra

Trabaja en la Unidad de Nutrición clínica y Dietética. Centro Médico de AsturiasProfesor asociado de la Universidad Europea del Atlántico, AYCAN



Miembro del Grupo Español de Dietistas/ Nutricionistas de Fibrosis Quística (GEDN/ FQ).

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Published

2017-04-04

How to Cite

Garriga, M., Horrisberger, A., Ruiz de las Heras de la Hera, A., Catalán, N., Fernández, G., Suárez, M., Porras, N., & Monje, L. (2017). Clinical Practice Guidelines for nutritional management of Cystic Fibrosis patients (GPC-CF). Spanish Journal of Human Nutrition and Dietetics, 21(1), 74–97. https://doi.org/10.14306/renhyd.21.1.229